Журнал болезней крови и переливания крови

Абстрактный

Isolated Factor VII Deficiency of Coagulation: A Case Diagnosed in the Departement of Onco-hematology of National Hospital of Niamey

Djibrilla Almoustapha A*, Abdou-Moussa H, Abba-Ousmane F, Abdoulaye-Soumana O, MalamAbdou B, Maman Brah M, Chefou M, Diori A

Factor VII deficiency is a rare coagulopathy that may be congenital or acquiered, the transmission of which is autosomal and recessive, due to a decrease or absence of factor VII in coagulation without impact on other factors. The prevalence is estimated at 1-2/1,000,000 inhabitants in France. Its clinical expression is polymorphic. We report the observation of a case of isolated factor VII deficiency in 10 years old child diagnosed with onco-hematologie department at the national hospital of Niamey.