Sarra Wang, Valerie Lan-Pak-Kee, Chhaya Sharma
Moyamoya (MM) is a rare cerebrovascular occlusive disease affecting the terminal portion of the internal carotid artery. It can be of primary idiopathic origin or secondary, where it is associated with other conditions such as Sickle Cell Disease (SCD). We present the anaesthetic management of a 16 year old female with SCD and MM undergoing a cerebral revascularisation procedure which was complicated by possible Central Diabetes Insipidus (CDI) intra-operatively. We hope to raise awareness of this rare disorder and add to the paucity of literature describing the anaesthetic management and potential peri-operative challenges posed by such patients.